Parry-Romberg syndrome: A linear variant of scleroderma with discoid lupus erythematosus on scalp - an association

Parry-Romberg Syndrome Associated with Localized Scleroderma

Parry-Romberg syndrome is a rare neurocutaneous disorder of unknown origin. It is characterized by progressive facial hemiatrophy and frequently overlaps with a condition known as linear scleroderma 'en coup de sabre'. Neurological involvement is frequently described in these patients, including migraine, facial pain and epilepsy, which represent the commonest neurological conditions, sometimes...

Parry Romberg syndrome with localized scleroderma: A case report

Parry Romberg syndrome(PRS) is a rare acquired poorly understood neurocutaneous syndrome of unknown etiology characterized by slow progressive atrophic changes commonly affecting one half of the face. The exact incidence and etiology towards the syndrome remains unclear. Apart from the multifactorial etiology proposed, the possible primary cause is mainly attributed to the cerebral disturbance ...

Linear cutaneous lupus erythematosus/discoid lupus erythematosus in an adult

Linear cutaneous lupus erythematosus (LCLE) is rare. The LCLE was proposed by Abe et al. [1] for discoid lupus erythematosus (DLE) with a linear configuration in 1988. It occurs mainly in children and young adults. Lesions appear as linear unilateral erythematous plaques following the Blaschko lines and are observed most frequently on the face, although the neck, trunk and extremities may also ...

Scalp sarcoidosis mimicking discoid lupus erythematosus with lichenoid features in histology

Parry Romberg syndrome: a close differential diagnosis of linear scleroderma en coup de sabre.

This 45 years old lady complained of asymmetry of her face since the age of 15 years. She also complained of decreased sweating on the left side and an intermittent left hemicranial headache. Examination revealed marked atrophy of the left side of the face involving the skin, subcutaneous tissue and muscles of the orbital, maxillary and mandibular regions. There was no induration or tightening ...